Demographics:
6 years old, Female
Indication:
Left greater than right sensorineural hearing loss
Findings
- LEFT
- Normal appearance of the external ear
- The incus appears fused to the lateral wall of the middle ear
- Patulous vestibule with assimilation of the lateral semicircular canal. The posterior and superior semicircular canals are normally formed without dehiscence
- Featureless, bulbous appearance of the cochlea with absent modiolus and internal partitioning
- RIGHT
- Normal appearance of the external and middle ear
- Patulous vestibule with assimilation of the lateral semicircular canal. The posterior and superior semicircular canals are normally formed without dehiscence
- Deficient modiolus with incomplete segmentation of the middle and apical turns of the cochlea
Diagnosis
Left cochlear incomplete partition type I (IP-I)
Key Imaging Features
Become a PRO member to unlock the key imaging features
Differential Diagnosis
Become a PRO member to unlock the differential diagnosis
Pearls
Become a PRO member to unlock the pearls
Discussion